Full Name
Mannosidase Beta Like

Keywords
Mannosidase Beta Like; Mannosidase, Beta A, Lysosomal-Like; Mannosidase Beta A Like

Background
This is a beta-mannosidase enzyme involved in the lysosomal degradation of N-linked glycans. It cleaves beta-mannosyl residues from oligosaccharides. Deficiency in a related beta-mannosidase causes beta-mannosidosis, a lysosomal storage disease, suggesting MANBAL may have specific substrates whose degradation is important for normal cellular function.
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