SIX Homeobox 5; DM Locus-Associated Homeodomain Protein; Sine Oculis Homeobox Homolog 5; DMAHP; Dystrophia Myotonica-Associated Homeodomain Protein; Sine Oculis Homeobox (Drosophila) Homolog 5; Sine Oculis Homeobox Homolog 5 (Drosophila); Homeobox Protein SIX5; BOR2

The protein encoded by this gene is a homeodomain-containing transcription factor that appears to function in the regulation of organogenesis. This gene is located downstream of the dystrophia myotonica-protein kinase gene. Mutations in this gene are a cause of branchiootorenal syndrome type 2.